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Immunodeficiencies
Metadata
Name | Immunodeficiencies |
Type | Disease or Syndrome |
Group | Haematological or immunological |
Data Sources |
|
Clinical Terminologies |
Read Version 2 ICD-10 |
Codelists | kuan_immunodef_F6u5wxYWxj4F6gFtp34TPq_Read2.csv kuan_immunodef_F6u5wxYWxj4F6gFtp34TPq_ICD10.csv |
Valid Event Data Range | 01/01/1999 - 01/07/2016 |
Sex |
Female Male |
Authors | Kuan V, Denaxas S, Gonzalez-Izquierdo A, Direk K, Bhatti O, Husain S, Sutaria S, Hingorani M, Nitsch D, Parisinos C, Lumbers T, Mathur R, Sofat R, Casas JP, Wong I, Hemingway H, Hingorani A |
Agreement Date | 20 May 2019 |
Version (UUID) | 1 (F6u5wxYWxj4F6gFtp34TPq) |
Primary care
Disease | Readcode | Medcode | ReadcodeDescr | Category |
---|---|---|---|---|
Immunodeficiencies | C390000 | 15137.0 | Hypogammaglobulinaemia NOS | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390100 | 8548.0 | Selective IgA immunodeficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390200 | 18701.0 | Selective IgM immunodeficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390300 | 18700.0 | Selective IgG immunodeficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390400 | 68440.0 | Other selective immunoglobulin deficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390500 | 57161.0 | Congenital hypogammaglobulinaemia | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390511 | 65603.0 | Bruton's agammaglobulinaemia | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390512 | 60880.0 | Congenital X-linked agammaglobulinaemia | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390600 | 69373.0 | Immunodeficiency with IgM hypergammaglobulinaemia | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390700 | 57322.0 | Common variable immunodeficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390800 | 92569.0 | Transient infant hypogammaglobulinaemia | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390900 | 62598.0 | Agammaglobulinaemia NEC | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390A00 | 69184.0 | Dysimmunoglobulinaemia NEC | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390A11 | 43653.0 | Dysgammaglobulinaemia NEC | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390B00 | 60026.0 | Antibod def wth nr-norm imunoglob/or wth hyperimunoglobaemia | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390.00 | 44147.0 | Deficiencies of humoral immunity | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390.11 | 35682.0 | Agammaglobulinaemia | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390y00 | 69854.0 | Other specified deficiency of humoral immunity | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C390z00 | 16295.0 | Deficiency of humoral immunity NOS | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C391000 | 50665.0 | Predominantly T-cell immuno-deficiency NOS | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C391011 | 48035.0 | T-lymphocyte deficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C391012 | 60758.0 | Cellular immunity syndrome | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C391100 | 10955.0 | Di George syndrome | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C391200 | 31322.0 | Wiskott - Aldrich syndrome | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C391211 | 42439.0 | Thrombocytopenic eczema with immunodeficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C391.00 | 48307.0 | Deficiencies of cell-mediated immunity | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C392100 | 48293.0 | Severe combined immunodeficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C392111 | 94120.0 | Swiss type agammaglobulinaemia | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C392300 | 31541.0 | Severe combined immunodefiency with reticular dysgenesis | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C392400 | 66073.0 | Severe combined immunodef with low T- and B-cell numbers | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C392500 | 49542.0 | Severe combined immunodef with low or normal B-cell numbers | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C392600 | 72804.0 | Adenosine deaminase deficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C392700 | 93936.0 | Purine nucleoside phosphorylase deficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C392800 | 50526.0 | Major histocompatibility complex class I deficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C392900 | 103977.0 | Major histocompatibility complex class II deficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C392.00 | 62236.0 | Combined immunity deficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C392z00 | 62328.0 | Combined immunity deficiency NOS | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C393.00 | 3129.0 | Unspecified immunity deficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C395.00 | 65617.0 | Immunodeficiency with short-limbed stature | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C396.00 | 56108.0 | Immunodef follow hereditary defect respon Epstein-Barr vir | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C397.00 | 54203.0 | Hyperimmunoglobulin E syndrome | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C398000 | 93892.0 | Com var immunodef with predom abn B-cell numbers and functns | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C398200 | 66857.0 | Common variable immunodef wth autoantibod to B- or T-cells | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C398.00 | 21975.0 | Common variable immunodeficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C39X.00 | 39800.0 | Immunodeficiency associated+major defect, unspecified | Diagnosis of Immunodeficiencies |
Immunodeficiencies | C39y000 | 54904.0 | Lymphocyte function antigen-1 defect | Diagnosis of Immunodeficiencies |
Immunodeficiencies | Cyu0000 | 106788.0 | [X]Other immunodeficiencies+predominantly antibody defects | Diagnosis of Immunodeficiencies |
Immunodeficiencies | Cyu0400 | 73131.0 | [X]Other common variable immunodeficiencies | Diagnosis of Immunodeficiencies |
Immunodeficiencies | Cyu0500 | 66386.0 | [X]Other specified immunodeficiency disorders | Diagnosis of Immunodeficiencies |
Secondary care
Diagnoses
Disease | ICD10code | ICD10codeDescr | Category |
---|---|---|---|
Immunodeficiencies | D80 | Immunodeficiency with predominantly antibody defects | Diagnosis of Immunodeficiencies |
Immunodeficiencies | D81 | Combined immunodeficiencies | Diagnosis of Immunodeficiencies |
Immunodeficiencies | D82 | Immunodeficiency associated with other major defects | Diagnosis of Immunodeficiencies |
Immunodeficiencies | D83 | Common variable immunodeficiency | Diagnosis of Immunodeficiencies |
Immunodeficiencies | D84.0 | Lymphocyte function antigen-1 [LFA-1] defect | Diagnosis of Immunodeficiencies |
Immunodeficiencies | D84.8 | Other specified immunodeficiencies | Diagnosis of Immunodeficiencies |
Immunodeficiencies | D84.9 | Immunodeficiency, unspecified | Diagnosis of Immunodeficiencies |
Implementation
At the specified date, a patient is defined as having had 'Immunodeficiencies' IF they meet the criteria for any of the following on or before the specified date. The earliest date on which the individual meets any of the following criteria on or before the specified date is defined as the first event date: Primary care 1. 'Immunodeficiencies' diagnosis or history of diagnosis during a consultation OR Secondary care (ICD10) 1. ALL diagnoses of 'Immunodeficiencies' or history of diagnosis during a hospitalization
Publications
Kuan V., Denaxas S., Gonzalez-Izquierdo A. et al. A chronological map of 308 physical and mental health conditions from 4 million individuals in the National Health Service. The Lancet Digital Health - DOI 10.1016/S2589-7500(19)30012-3